4-Methylumbelliferyl-6-sulfo-N-acetyl-?-D-glucosaminide, Potassium Salt

4-Methylumbelliferyl-6-sulfo-N-acetyl-?-D-glucosaminide, Potassium Salt, Fluorogenic substrate for isoenzyme A of N-acetyl-?-D-glucosaminidase (hexosaminidase A). Can be used for the prenatal diagnosis of Tay-Sachs disease and for the classification of GM2 gangliosidosis genotypes.